| U1 small nuclear ribonucleoprotein C (U1 snRNP C) (U1-C) (U1C) | SNRPC hCG_16077 | Q5TAL4 | 3 |
| U3 small nucleolar RNA-associated protein 14 homolog C | UTP14C KIAA0266 | Q5TAP6 | 3 |
| U3 small nucleolar RNA-associated protein 6 homolog (Hepatocellular carcinoma-associated antigen 66) (Multiple hat domains protein) | UTP6 C17orf40 HCA66 MHAT | Q9NYH9 | 3 |
| U5 small nuclear ribonucleoprotein 40 kDa protein (U5 snRNP 40 kDa protein) (U5-40K) (38 kDa-splicing factor) (Prp8-binding protein) (hPRP8BP) (U5 snRNP-specific 40 kDa protein) (WD repeat-containing protein 57) | SNRNP40 PRP8BP SFP38 WDR57 | Q96DI7 | 3 |
| U7 snRNA-associated Sm-like protein LSm10 | LSM10 | Q969L4 | 3 |
| Ubiquilin-2 (Chap1) (DSK2 homolog) (Protein linking IAP with cytoskeleton 2) (PLIC-2) (hPLIC-2) (Ubiquitin-like product Chap1/Dsk2) | UBQLN2 N4BP4 PLIC2 HRIHFB2157 | Q9UHD9 | 3 |
| Ubiquinol-cytochrome c reductase complex chaperone CBP3 homolog (Basic FGF-repressed Zic-binding protein) (bFGF-repressed Zic-binding protein) (bFZb) | UQCC BZFB C20orf44 | Q9NVA1 | 3 |
| Ubiquinone biosynthesis protein COQ7 homolog (Coenzyme Q biosynthesis protein 7 homolog) (Timing protein clk-1 homolog) | COQ7 | Q99807 | 3 |
| Ubiquitin carboxyl-terminal hydrolase 11 (EC 3.4.19.12) (Deubiquitinating enzyme 11) (Ubiquitin thioesterase 11) (Ubiquitin-specific-processing protease 11) | USP11 UHX1 | P51784 | 3 |
| Ubiquitin carboxyl-terminal hydrolase 12 (EC 3.4.19.12) (Deubiquitinating enzyme 12) (Ubiquitin thioesterase 12) (Ubiquitin-hydrolyzing enzyme 1) (Ubiquitin-specific-processing protease 12) | USP12 UBH1 USP12L1 | O75317 | 3 |
| Ubiquitin carboxyl-terminal hydrolase 25 (EC 3.4.19.12) (Deubiquitinating enzyme 25) (USP on chromosome 21) (Ubiquitin thioesterase 25) (Ubiquitin-specific-processing protease 25) | USP25 USP21 | Q9UHP3 | 3 |
| Ubiquitin carboxyl-terminal hydrolase 48 (EC 3.4.19.12) (Deubiquitinating enzyme 48) (Ubiquitin thioesterase 48) (Ubiquitin-specific-processing protease 48) | USP48 USP31 | Q86UV5 | 3 |
| Ubiquitin carboxyl-terminal hydrolase 6 (EC 3.4.19.12) (Deubiquitinating enzyme 6) (Proto-oncogene TRE-2) (Ubiquitin thioesterase 6) (Ubiquitin-specific-processing protease 6) | USP6 HRP1 TRE2 | P35125 | 3 |
| Ubiquitin carboxyl-terminal hydrolase isozyme L1 (UCH-L1) (EC 3.4.19.12) (EC 6.-.-.-) (Neuron cytoplasmic protein 9.5) (PGP 9.5) (PGP9.5) (Ubiquitin thioesterase L1) | UCHL1 | P09936 | 3 |
| Ubiquitin-associated protein 1 (UBAP-1) (Nasopharyngeal carcinoma-associated gene 20 protein) | UBAP1 NAG20 | Q9NZ09 | 3 |
| Ubiquitin-conjugating enzyme E2 D1 (EC 6.3.2.19) (Stimulator of Fe transport) (SFT) (UBC4/5 homolog) (UbcH5) (Ubiquitin carrier protein D1) (Ubiquitin-conjugating enzyme E2(17)KB 1) (Ubiquitin-conjugating enzyme E2-17 kDa 1) (Ubiquitin-protein ligase D1) | UBE2D1 SFT UBC5A UBCH5 UBCH5A | P51668 | 3 |
| Ubiquitin-conjugating enzyme E2 J1 (EC 6.3.2.19) (Non-canonical ubiquitin-conjugating enzyme 1) (NCUBE-1) (Yeast ubiquitin-conjugating enzyme UBC6 homolog E) (HsUBC6e) | UBE2J1 NCUBE1 CGI-76 HSPC153 HSPC205 | Q9Y385 | 3 |
| Ubiquitin-conjugating enzyme E2 variant 3 (UEV-3) (EV and lactate/malate dehydrogenase domain-containing protein) | UEVLD UEV3 | Q8IX04 | 3 |
| Ubiquitin-like domain-containing CTD phosphatase 1 (EC 3.1.3.16) (Nuclear proteasome inhibitor UBLCP1) | UBLCP1 | Q8WVY7 | 3 |
| Ubiquitin-like modifier-activating enzyme ATG7 (ATG12-activating enzyme E1 ATG7) (Autophagy-related protein 7) (APG7-like) (hAGP7) (Ubiquitin-activating enzyme E1-like protein) | ATG7 APG7L | O95352 | 3 |
| UDP galactose 4'-epimerase (EC 5.1.3.2) (cDNA, FLJ95174, highly similar to Homo sapiens galactose-4-epimerase, UDP- (GALE), mRNA) | GALE | Q38G75 | 3 |
| UDP-GlcNAc:betaGal beta-1,3-N-acetylglucosaminyltransferase 8 (BGnT-8) (Beta-1,3-Gn-T8) (Beta-1,3-N-acetylglucosaminyltransferase 8) (Beta3Gn-T8) (EC 2.4.1.-) | B3GNT8 B3GALT7 BGALT15 | Q7Z7M8 | 3 |
| UDP-glucuronosyltransferase 1-6 (UDPGT 1-6) (UGT1*6) (UGT1-06) (UGT1.6) (EC 2.4.1.17) (Phenol-metabolizing UDP-glucuronosyltransferase) (UDP-glucuronosyltransferase 1-F) (UGT-1F) (UGT1F) (UDP-glucuronosyltransferase 1A6) | UGT1A6 GNT1 UGT1 | P19224 | 3 |
| UDP-glucuronosyltransferase 2B17 (UDPGT 2B17) (EC 2.4.1.17) (C19-steroid-specific UDP-glucuronosyltransferase) (C19-steroid-specific UDPGT) | UGT2B17 | O75795 | 3 |
| UDP-N-acetylglucosamine/UDP-glucose/GDP-mannose transporter (Homolog of Fringe connection protein 1) (HFRC1) (SQV7-like protein) (SQV7L) (Solute carrier family 35 member D2) (UDP-galactose transporter-related protein 8) (UGTrel8) | SLC35D2 HFRC UGTREL8 | Q76EJ3 | 3 |
| UDP-N-acetylhexosamine pyrophosphorylase (Antigen X) (AGX) (Sperm-associated antigen 2) [Includes: UDP-N-acetylgalactosamine pyrophosphorylase (EC 2.7.7.83) (AGX-1); UDP-N-acetylglucosamine pyrophosphorylase (EC 2.7.7.23) (AGX-2)] | UAP1 SPAG2 | Q16222 | 3 |
| UDP-xylose and UDP-N-acetylglucosamine transporter (Solute carrier family 35 member B4) (YEA4 homolog) | SLC35B4 YEA4 PSEC0055 | Q969S0 | 3 |
| Uncharacterized aarF domain-containing protein kinase 4 (EC 2.7.11.-) | ADCK4 | Q96D53 | 3 |
| Uncharacterized protein C11orf35 | C11orf35 | Q8IXW0 | 3 |
| Uncharacterized protein C11orf57 | C11orf57 | Q6ZUT1 | 3 |
| Uncharacterized protein C12orf43 | C12orf43 | Q96C57 | 3 |
| Uncharacterized protein C14orf142 | C14orf142 | Q9BXV9 | 3 |
| Uncharacterized protein C14orf93 | C14orf93 | Q9H972 | 3 |
| Uncharacterized protein C15orf57 (Protein CCDC32) | C15orf57 CCDC32 | Q9BV29 | 3 |
| Uncharacterized protein C16orf59 | C16orf59 | Q7L2K0 | 3 |
| Uncharacterized protein C17orf74 | C17orf74 | Q0P670 | 3 |
| Uncharacterized protein C17orf99 | C17orf99 UNQ464/PRO809 | Q6UX52 | 3 |
| Uncharacterized protein C19orf47 | C19orf47 | Q8N9M1 | 3 |
| Uncharacterized protein C1orf115 | C1orf115 | Q9H7X2 | 3 |
| Uncharacterized protein C1orf50 | C1orf50 | Q9BV19 | 3 |
| Uncharacterized protein C21orf59 | C21orf59 C21orf48 | P57076 | 3 |
| Uncharacterized protein C21orf62 (B37) | C21orf62 C21orf120 | Q9NYP8 | 3 |
| Uncharacterized protein C3orf33 | C3orf33 MSTP052 | Q6P1S2 | 3 |
| Uncharacterized protein C9orf114 | C9orf114 | Q5T280 | 3 |
| Uncharacterized protein KIAA0513 | KIAA0513 | O60268 | 3 |
| Uncharacterized protein KIAA1522 | KIAA1522 | Q9P206 | 3 |
| Uncharacterized protein KIAA1683 | KIAA1683 | Q9H0B3 | 3 |
| Undifferentiated embryonic cell transcription factor 1 | UTF1 | Q5T230 | 3 |
| UPF0249 protein ydjC homolog | YDJC | A8MPS7 | 3 |
| UPF0317 protein C14orf159, mitochondrial | C14orf159 UNQ2439/PRO5000 | Q7Z3D6 | 3 |
| UPF0500 protein C1orf216 | C1orf216 | Q8TAB5 | 3 |
| UPF0536 protein C12orf66 | C12orf66 | Q96MD2 | 3 |
| UPF0545 protein C22orf39 | C22orf39 | Q6P5X5 | 3 |
| UPF0552 protein C15orf38 | C15orf38 | Q7Z6K5 | 3 |
| UPF0554 protein C2orf43 | C2orf43 | Q9H6V9 | 3 |
| UPF0562 protein C7orf55 | C7orf55 HSPC268 | Q96HJ9 | 3 |
| UPF0565 protein C2orf69 | C2orf69 | Q8N8R5 | 3 |
| UPF0690 protein C1orf52 (BCL10-associated gene protein) | C1orf52 BAG GM117 | Q8N6N3 | 3 |
| UPF0696 protein C11orf68 (Basophilic leukemia-expressed protein Bles03) (Protein p5326) | C11orf68 BLES03 | Q9H3H3 | 3 |
| UPF0711 protein C18orf21 (HBV X-transactivated gene 13 protein) (HBV XAg-transactivated protein 13) | C18orf21 XTP13 PNAS-124 PNAS-131 | Q32NC0 | 3 |
| Uracil nucleotide/cysteinyl leukotriene receptor (UDP/CysLT receptor) (G-protein coupled receptor 17) (P2Y-like receptor) (R12) | GPR17 | Q13304 | 3 |
| Uroplakin-1a (UP1a) (Tetraspanin-21) (Tspan-21) (Uroplakin Ia) (UPIa) (UPKa) | UPK1A TSPAN21 | O00322 | 3 |
| Uteroglobin (Clara cell phospholipid-binding protein) (CCPBP) (Clara cells 10 kDa secretory protein) (CC10) (Secretoglobin family 1A member 1) (Urinary protein 1) (UP-1) (UP1) (Urine protein 1) | SCGB1A1 CC10 CCSP UGB | P11684 | 3 |
| V-akt murine thymoma viral oncogene homolog 1 (V-akt murine thymoma viral oncogene homolog 1, isoform CRA_a) | AKT1 hCG_96740 | B0LPE5 | 3 |
| V-raf-1 murine leukemia viral oncogene homolog 1 | RAF1 | L7RRS6 | 3 |
| V-set and immunoglobulin domain-containing protein 10-like | VSIG10L | Q86VR7 | 3 |
| V-set and immunoglobulin domain-containing protein 2 (Cortical thymocyte-like protein) (CT-like protein) | VSIG2 CTH CTXL UNQ2770/PRO7154 | Q96IQ7 | 3 |
| V-set and transmembrane domain-containing protein 2B | VSTM2B | A6NLU5 | 3 |
| V-type proton ATPase subunit d 2 (V-ATPase subunit d 2) (Vacuolar proton pump subunit d 2) | ATP6V0D2 | Q8N8Y2 | 3 |
| V-type proton ATPase subunit S1 (V-ATPase subunit S1) (Protein XAP-3) (V-ATPase Ac45 subunit) (V-ATPase S1 accessory protein) (Vacuolar proton pump subunit S1) | ATP6AP1 ATP6IP1 ATP6S1 VATPS1 XAP3 | Q15904 | 3 |
| Vacuolar protein sorting-associated protein 11 homolog (hVPS11) (RING finger protein 108) | VPS11 RNF108 PP3476 | Q9H270 | 3 |
| Vacuolar protein sorting-associated protein 18 homolog (hVPS18) | VPS18 KIAA1475 | Q9P253 | 3 |
| Vacuolar protein sorting-associated protein 26B (Vesicle protein sorting 26B) | VPS26B | Q4G0F5 | 3 |
| Vacuolar protein sorting-associated protein 37B (hVps37B) (ESCRT-I complex subunit VPS37B) | VPS37B | Q9H9H4 | 3 |
| Vacuolar protein sorting-associated protein 52 homolog (SAC2 suppressor of actin mutations 2-like protein) | VPS52 SACM2L | Q8N1B4 | 3 |
| Vacuolar protein sorting-associated protein 8 homolog | VPS8 KIAA0804 | Q8N3P4 | 3 |
| Vacuolar protein-sorting-associated protein 25 (hVps25) (Dermal papilla-derived protein 9) (ELL-associated protein of 20 kDa) (ESCRT-II complex subunit VPS25) | VPS25 DERP9 EAP20 | Q9BRG1 | 3 |
| Vacuolar protein-sorting-associated protein 36 (ELL-associated protein of 45 kDa) (ESCRT-II complex subunit VPS36) | VPS36 C13orf9 EAP45 CGI-145 | Q86VN1 | 3 |
| Vam6/Vps39-like protein (TRAP1-like protein) (hVam6p) | VPS39 KIAA0770 TLP VAM6 | Q96JC1 | 3 |
| Variable charge X-linked protein 2 (Variable charge protein on X with two repeats) (VCX-2r) (Variably charged protein X-B) (VCX-B) | VCX2 VCX2R VCXB | Q9H322 | 3 |
| Vascular endothelial growth factor B (Vascular endothelial growth factor B isoform VEGF-B186) | VEGFB | Q7LAP4 | 3 |
| Vasoactive intestinal polypeptide receptor 1 (VIP-R-1) (Pituitary adenylate cyclase-activating polypeptide type II receptor) (PACAP type II receptor) (PACAP-R-2) (PACAP-R2) (VPAC1) | VIPR1 | P32241 | 3 |
| Vasopressin-neurophysin 2-copeptin (AVP-NPII) [Cleaved into: Arg-vasopressin (Arginine-vasopressin); Neurophysin 2 (Neurophysin-II); Copeptin] | AVP ARVP VP | P01185 | 3 |
| Ventral anterior homeobox 2 | VAX2 | F1T0K5 | 3 |
| Very-long-chain (3R)-3-hydroxyacyl-[acyl-carrier protein] dehydratase 4 (EC 4.2.1.134) (3-hydroxyacyl-CoA dehydratase 4) (HACD4) (Protein tyrosine phosphatase-like protein PTPLAD2) (Protein-tyrosine phosphatase-like A domain-containing protein 2) | PTPLAD2 HACD4 | Q5VWC8 | 3 |
| Vesicle transport protein SFT2C (SFT2 domain-containing protein 3) | SFT2D3 | Q587I9 | 3 |
| Vesicle transport protein USE1 (Putative MAPK-activating protein PM26) (USE1-like protein) (p31) | USE1 USE1L MDS032 | Q9NZ43 | 3 |
| Vesicle-associated membrane protein-associated protein B/C (VAMP-B/VAMP-C) (VAMP-associated protein B/C) (VAP-B/VAP-C) | VAPB UNQ484/PRO983 | O95292 | 3 |
| Vesicular integral-membrane protein VIP36 (Glycoprotein GP36b) (Lectin mannose-binding 2) (Vesicular integral-membrane protein 36) (VIP36) | LMAN2 C5orf8 | Q12907 | 3 |
| Vitamin D nuclear receptor variant 1 | NR1i1 | F1D8P8 | 3 |
| Vitamin D3 receptor (VDR) (1,25-dihydroxyvitamin D3 receptor) (Nuclear receptor subfamily 1 group I member 1) | VDR NR1I1 | P11473 | 3 |
| Vitamin K-dependent gamma-carboxylase (EC 4.1.1.90) (Gamma-glutamyl carboxylase) (Peptidyl-glutamate 4-carboxylase) (Vitamin K gamma glutamyl carboxylase) | GGCX GC | P38435 | 3 |
| Voltage-dependent calcium channel gamma-8 subunit (Neuronal voltage-gated calcium channel gamma-8 subunit) (Transmembrane AMPAR regulatory protein gamma-8) (TARP gamma-8) | CACNG8 CACNG6 | Q8WXS5 | 3 |
| Voltage-dependent calcium channel gamma-like subunit (Neuronal voltage-gated calcium channel gamma-like subunit) (Transmembrane protein 37) | TMEM37 PR | Q8WXS4 | 3 |
| Voltage-dependent calcium channel subunit alpha-2/delta-1 (Voltage-gated calcium channel subunit alpha-2/delta-1) [Cleaved into: Voltage-dependent calcium channel subunit alpha-2-1; Voltage-dependent calcium channel subunit delta-1] | CACNA2D1 CACNL2A CCHL2A MHS3 | P54289 | 3 |
| Voltage-dependent L-type calcium channel subunit beta-2 (CAB2) (Calcium channel voltage-dependent subunit beta 2) (Lambert-Eaton myasthenic syndrome antigen B) (MYSB) | CACNB2 CACNLB2 MYSB | Q08289 | 3 |
| WAP, Kazal, immunoglobulin, Kunitz and NTR domain-containing protein 2 (Growth and differentiation factor-associated serum protein 1) (GASP-1) (hGASP-1) (WAP, follistatin, immunoglobulin, Kunitz and NTR domain-containing-related protein) (WFIKKN-related protein) | WFIKKN2 GASP1 WFIKKNRP UNQ9235/PRO31996 | Q8TEU8 | 3 |
| WD repeat-containing protein 41 | WDR41 MSTP048 | Q9HAD4 | 3 |
| WD repeat-containing protein 5 (BMP2-induced 3-kb gene protein) | WDR5 BIG3 | P61964 | 3 |
| WD repeat-containing protein 59 | WDR59 KIAA1923 FP977 | Q6PJI9 | 3 |